Sassoon Hospital operates baby with rare blood clot disorder

Nine-month-old Mihir Deshmane, suffering from factor seven deficiency, underwent hernia operation on Thursday last. Globally, only 200 cases of Factor seven deficiency are reported. The blood clotting agent called factor seven is absent in his body since birth. And the doctors, with continuous monitoring of factor seven supplementation, performed the operation

assoon Hospital operates baby with rare blood clot disorder

A nine-month-old Mihir Deshmane, who hails from Pune, is suffering from a rarest form of blood clotting disorder called factor seven deficiency. Globally, only 200 cases of Factor seven deficiency are reported. On Thursday, the doctors at Sassoon hospital operated on Mihir’s hernia by supplementing him with factor seven.

Mihir has not taken any injection once in his life. His parents have been ensured that he will not get even a single scratch on his body. This rare blood disorder would cause Mihir excessive bleeding after an injury or surgery, as the blood clotting agent called factor seven is absent in his body since birth.

The Public Health Department of government of Maharashtra specially procured factor seven for Mihir’s surgery. Doctors, with continuous monitoring of factor seven supplementation, performed the operation.

Dr Minakshi Bhosale, pediatric surgeon at Sassoon, said, “When the child was two months old, he had come with obstructed inguinal hernia. We had operated him as that time there were chances of his bowel becoming gangrenous. We did not operate on the left-side hernia as we wanted to observe the healing of wound on the right side first. When the first operation was successful, we performed the second surgery last Thursday.”

Managing the dosage factor seven was a challenge for the doctors. Dr Sonali Salvi, associate professor at BJ Medical’s Sassoon hospital, said, “After every four hours, we were doing blood test to know if the blood is clotting properly or not. According to which, we were administering the factor seven to the patient. Managing the patient intra and post operatively was the most challenging factor, as mismanagement could have led to excessive bleeding and could have been risky.”

Rajesh Kulkarni, associate professor at Sassoon hospital said, “Factor seven is very rare as only 200 cases have been reported so far, and its procurement is difficult for private hospitals. The tough task in the surgery was administering and monitoring the factor seven to the baby.” Kalpana Kulkarni, associate professor at Sassoon hospital was also part of the team which operated on the patient.

After the first operation done six months ago, he was operated for the second time on Thursday. The patient was discharged on Tuesday. “Many private hospitals in the city had denied treatment to him and had even given us in writing that he cannot be treated. But we are very grateful for Sassoon who helped our son,” said Vaishali Deshmane, Mihir’s mother.